Retina-Vitreous
2012 , Vol 20 , Num 2
Two Siblings with Juvenile X-Linked Retinoschisis
1M.D. Asistant, İnönü University Faculity of Medicine, Department of Ophthalmology, Malatya/TURKEY2M.D. Asistant Professor, İnönü University Faculity of Medicine, Department of Ophthalmology, Malatya/TURKEY
3M.D. Professor, İnönü University Faculity of Medicine, Department of Ophthalmology, Malatya/TURKEY X-linked juvenile retinoschisis (XLRS) is a congenital ocular disease that occurs early in life and shows bilateral behavior. The disease mostly affects men because of X-linked hereditary transition. It has typical ophthalmoscopic and electrophysiological findings and the main findings are maculopathy and peripheral retinoschisis. In this study, two brothers with XLRS and the current developments related to management of the disease are presented. Keywords : X-linked juvenile retinoschisis, foveal schisis, peripheral retinoschisis